Abstract

A 55-year-old male patient with Sturge-Weber syndrome (SWeS) and obesity hypoventilation syndrome (OHS) was counselled to continue with Continuous Positive Airway Pressure (CPAP) with 10 cmH2O in perioperative period, including on morning of surgery. Before surgery, intramuscular clonidine 2 mcg/kg was administered. During intraoperative setting, we opted for intubation underwent awake fiberoptic intubation guidance with application of High Flow Nasal Oxygen (HFNO). General anaesthesia was induced with target-controlled infusion of propofol and remifentanil after check correct position of tracheal tube, and stopped respectively 10 and 5 minutes prior to extubating assessment. In post-anaesthesia care unit, we observed an intolerance to CPAP due discomfort with desaturation until to SPO2 80%: we have administrated HFNO titrated between 50-70 l/min, FiO2 60-80 % by nasal cannula with an improvement in 3 minutes until to normal value (>94%). After 24 h, monitoring of vital parameters discharge criteria were met, patient was reassessed.

Brief Summary

The manuscript would to contribute to reporting the perioperative management of a clinical case of a patient suffering from SturgeWeber syndrome (SWeS) and obesity hypoventilation syndrome (OHS) compliant to ventilation undergoing a maxillofacial surgery procedure. Anaesthesiologic management of patients with SWeS and OHS require a comprehensive to improve long-term clinical outcomes.